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KMID : 0882420110800040453
Korean Journal of Medicine
2011 Volume.80 No. 4 p.453 ~ p.457
A Case of Intrahepatic Sarcomatoid Cholangiocarcinoma with Rhabdoid Transformation
Kim Wan-Soo

Kim Tae-Hyo
Hwang Jae-Jin
Kim Hyun-Jin
Jung Woon-Tae
Lee Ok-Jae
Lee Jeong-Hee
Abstract
Rhabdoid transformation is an extremely rare occurrence in sarcomatoid cholangiocarcinoma. Only two cases have been reported in the medical literature worldwide, and its clinical and pathological characteristics remain unknown. Published case reports indicate that rhabdoid cholangiocarcinoma grows rapidly, with early metastasis and a particularly poor prognosis. Here, we report a case of rhabdoid transformation in sarcomatoid cholangiocarcinoma that exhibited aggressive behavior and resulted in a devastating prognosis.
KEYWORD
Rhabdoid, Sarcomatoid, Cholangiocarcinoma
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